Transfusion-associated graft-versus-host disease in severe combined immunodeciency
dc.contributor.buuauthor | Kılıç, Sara Şebnem | |
dc.contributor.buuauthor | Kavurt, Sumru | |
dc.contributor.buuauthor | Adım, Şaduman Balaban | |
dc.contributor.department | Uludağ Üniversitesi/Tıp Fakültesi/Çocuk Sağlığı ve Hastalıkları Anabilim Dalı. | tr_TR |
dc.contributor.department | Uludağ Üniversitesi/Tıp Fakültesi/Tıbbi Patoloji Anabilim Dalı. | tr_TR |
dc.contributor.orcid | 0000-0001-8571-2581 | tr_TR |
dc.contributor.researcherid | AAH-1658-2021 | tr_TR |
dc.contributor.scopusid | 34975059200 | tr_TR |
dc.contributor.scopusid | 36127402300 | tr_TR |
dc.contributor.scopusid | 15730076300 | tr_TR |
dc.date.accessioned | 2021-12-30T12:28:08Z | |
dc.date.available | 2021-12-30T12:28:08Z | |
dc.date.issued | 2010 | |
dc.description.abstract | Transfusion-associated graft-versus-host disease (TA-GVHD) is a rare complication of cellular blood component transfusion that produces a graft-versus-host clinical picture with concomitant bone marrow aplasia. We report the case of 2 patients with severe combined immunodeficiency (SCID) who developed TA-GvHD. Both patients had been given nonirradiated erythrocyte suspension before the diagnosis of SCID. Although one of them was aged 12 months, he had still not been diagnosed as having severe T-cell deficiency at the time of transfusion. Both patients presented similar signs and symptoms (fever, skin rash, diarrhea, pancytopenia, and icterus). Skin biopsies demonstrated Grade II GVHD involvement. In both cases, sepsis and septic shock developed, with progression to multiorgan failure. Unfortunately, the 2 patients died, despite prompt, appropriate sepsis treatment and immunomodulatory therapy. TA-GVHD must be considered in the differential diagnosis of patients who present fever, pancytopenia, diarrhea, skin rash and icterus, and the transfusion history must be questioned. | en_US |
dc.identifier.citation | Kılıç, S. Ş. vd. (2010). "Transfusion-associated graft-versus-host disease in severe combined immunodeciency". Journal of Investigational Allergology and Clinical Immunology, 20(2), 153-156. | en_US |
dc.identifier.endpage | 156 | tr_TR |
dc.identifier.issn | 1018-9068 | |
dc.identifier.issue | 2 | tr_TR |
dc.identifier.pubmed | 20461970 | tr_TR |
dc.identifier.scopus | 2-s2.0-77953630982 | tr_TR |
dc.identifier.startpage | 153 | tr_TR |
dc.identifier.uri | http://hdl.handle.net/11452/23771 | |
dc.identifier.volume | 20 | tr_TR |
dc.identifier.wos | 000277247900008 | tr_TR |
dc.indexed.pubmed | Pubmed | en_US |
dc.indexed.scopus | Scopus | en_US |
dc.indexed.wos | SCIE | en_US |
dc.language.iso | en | en_US |
dc.publisher | Esmon Publicidad | en_US |
dc.relation.journal | Journal of Investigational Allergology and Clinical Immunology | en_US |
dc.relation.publicationcategory | Makale - Uluslararası Hakemli Dergi | tr_TR |
dc.rights | info:eu-repo/semantics/closedAccess | en_US |
dc.subject | Transfusion-associated graft-versus-host disease | en_US |
dc.subject | Severe combined immunodeficiency | en_US |
dc.subject | Irradiation | en_US |
dc.subject | Skin biopsy | en_US |
dc.subject | Fatal graft | en_US |
dc.subject | Deficiency | en_US |
dc.subject | Blood | en_US |
dc.subject | Allergy | en_US |
dc.subject | Immunology | en_US |
dc.subject.emtree | Aminotransferase | en_US |
dc.subject.emtree | Amphotericin B | en_US |
dc.subject.emtree | Antibiotic agent | en_US |
dc.subject.emtree | Cefepime | en_US |
dc.subject.emtree | Cyclosporin | en_US |
dc.subject.emtree | Fluconazole | en_US |
dc.subject.emtree | Fresh frozen plasma | en_US |
dc.subject.emtree | Gamma glutamyltransferase | en_US |
dc.subject.emtree | Ganciclovir | en_US |
dc.subject.emtree | Granulocyte colony stimulating factor | en_US |
dc.subject.emtree | Immunoglobulin | en_US |
dc.subject.emtree | Meropenem | en_US |
dc.subject.emtree | Methylprednisolone | en_US |
dc.subject.emtree | Teicoplanin | en_US |
dc.subject.emtree | Thymocyte antibody | en_US |
dc.subject.emtree | Aminotransferase blood level | en_US |
dc.subject.emtree | Article | en_US |
dc.subject.emtree | Bacterium culture | en_US |
dc.subject.emtree | Case report | en_US |
dc.subject.emtree | Cell suspension | en_US |
dc.subject.emtree | Child | en_US |
dc.subject.emtree | Death | en_US |
dc.subject.emtree | Diarrhea | en_US |
dc.subject.emtree | Drug megadose | en_US |
dc.subject.emtree | Erythrocyte concentrate | en_US |
dc.subject.emtree | Erythrocyte transfusion | en_US |
dc.subject.emtree | Febrile neutropenia | en_US |
dc.subject.emtree | Fever | en_US |
dc.subject.emtree | Human | en_US |
dc.subject.emtree | Human cell | en_US |
dc.subject.emtree | Human tissue | en_US |
dc.subject.emtree | Immunoglobulin deficiency | en_US |
dc.subject.emtree | Infant | en_US |
dc.subject.emtree | Infection | en_US |
dc.subject.emtree | Jaundice | en_US |
dc.subject.emtree | Klebsiella pneumoniae infection | en_US |
dc.subject.emtree | Laboratory test | en_US |
dc.subject.emtree | Male | en_US |
dc.subject.emtree | Mucosa inflammation | en_US |
dc.subject.emtree | Multiple organ failure | en_US |
dc.subject.emtree | Mycosis | en_US |
dc.subject.emtree | Pancytopenia | en_US |
dc.subject.emtree | Preschool child | en_US |
dc.subject.emtree | Rash | en_US |
dc.subject.emtree | Respiratory tract infection | en_US |
dc.subject.emtree | Sepsis | en_US |
dc.subject.emtree | Septic shock | en_US |
dc.subject.emtree | Severe combined immunodeficiency | en_US |
dc.subject.emtree | Skin biopsy | en_US |
dc.subject.emtree | Transfusion associated graft versus host disease | en_US |
dc.subject.emtree | Virus infection | en_US |
dc.subject.emtree | Early diagnosis | en_US |
dc.subject.emtree | Erythrocyte transfusion | en_US |
dc.subject.emtree | Fatality | en_US |
dc.subject.emtree | Graft versus host reaction | en_US |
dc.subject.emtree | Immunology | en_US |
dc.subject.emtree | Pathology | en_US |
dc.subject.emtree | Pathophysiology | en_US |
dc.subject.emtree | Recurrent disease | en_US |
dc.subject.emtree | Respiratory tract infection | en_US |
dc.subject.emtree | Severe combined immunodeficiency | en_US |
dc.subject.emtree | Skin | en_US |
dc.subject.mesh | Early diagnosis | en_US |
dc.subject.mesh | Erythrocyte transfusion | en_US |
dc.subject.mesh | Exanthema | en_US |
dc.subject.mesh | Fatal outcome | en_US |
dc.subject.mesh | Graft vs host disease | en_US |
dc.subject.mesh | Humans | en_US |
dc.subject.mesh | Infant | en_US |
dc.subject.mesh | Male | en_US |
dc.subject.mesh | Multiple organ failure | en_US |
dc.subject.mesh | Recurrence | en_US |
dc.subject.mesh | Respiratory tract infections | en_US |
dc.subject.mesh | Severe combined immunodeficiency | en_US |
dc.subject.mesh | Shock, septic | en_US |
dc.subject.mesh | Skin | en_US |
dc.subject.scopus | Transfusion; Graft Vs Host Disease; Blood Banks | en_US |
dc.subject.wos | Allergy | en_US |
dc.subject.wos | Immunology | en_US |
dc.title | Transfusion-associated graft-versus-host disease in severe combined immunodeciency | en_US |
dc.type | Article | |
dc.wos.quartile | Q3 (Allergy) | en_US |
dc.wos.quartile | Q4 (Immunology) | en_US |
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